Orthopedics synovial chondromatosis of the shoulder is rare. A site in the elbow was first reported in 1918 by henderson, but any joint may be. Primary synovial chondromatosis radiology reference article. Chondrosarcoma secondary to synovial chondromatosis. Jul 31, 2019 the role of hip arthroscopy in the condromatois of synovial disorders and loose bodies. Case repository synovial chondromatosis of the elbow with asymptomatic ulnar nerve compression jonathan m. The relative value of computed tomography ct in the. Synovial osteochondromatosis an overview sciencedirect. Synovial chondromatosis is a rare benign condition involving the synovial lining of joints, synovial sheaths and bursae. It can occur in a number of different joints in the human body, but most commonly occurs at the hip.
Synovial osteochondromatosis leads to pain in the affected joint as well as limitation of the range of motion. Synovial chondromatosis is an infrequent disease, who was first described according to ginaldi 1in by ambrosio pare. Common sites of synovial chondromatosis are the large joints such as the knee, elbow, hip, and shoulder. These nodules may extrude from the synovium and become loose. Mar 22, 2020 synovial chondromatosis of the temporomandibular joint. Synovial chondromatosis of the temporomandibular joint presenting as an intracranial mass louis a.
Synovial chondroma definition of synovial chondroma by. Synovial chondromatosis can arise in any joint in the body, but most commonly occurs in the knee. These foci can form free bodies and lead to mechanical arthrosis. Operative treatment of primary synovial osteochondromatosis of. A few weeks later his pain was decreased but never finished. Diagnosis depends on the clinical circumstances of the case and a radiologic interpretation which can exclude soft tissue tumors with calcifications and other malignant tumors characterized by the presence of multiple osteocartilaginous bodies. Hip resurfacing as treatment for synovial chondromatosis. It mainly affects large joints such as knee, hip, shoulder, and elbow, commonly in male patients. A disorder of a joint featuring a change of the normal joint lining synovium tissues cellular structure to form cartilage tissue. For language access assistance, contact the ncats public information officer. Synovial chondromatosis is a rare condition of metaplastic cartilage development in the synovial membrane of joints. Primary synovial chondromatosis sc is a rare proliferative disorder that causes pain, swelling, and restriction of movement to the joints it affects.
Synovial osteochondromatosis in the knee joint is rarely a confusing diagnostic problem. The disease is characteristically monoarticular, most commonly involving the knee. Since the mid 1950s, the technical strategy has included open arthrotomy with removal of loose bodies and synovectomy. Revision arthroscopic surgery for synovial chondromatosis of the hip. Computed tomography feature of synovial osteochondromatosis.
Pdf synovial chondromatosis is an uncommon disease characterised by foci of cartilage in the synovial tissue of joints, due to metaplasia of. Abstract primary synovial chondromatosis is a rare benign neoplastic process which affects. Primary synovial chondromatosis radiology reference. Synovial chondromatosis, chondrosarcoma, malignant transformation, osteochondromatosis, size. Synovial chondromatosis radiology reference article. The pain, swelling, and mechanical symptoms of synovial chondromatosis and its generation of loose bodies have historically been treated with surgery. Synovial osteochondromatosis is a rare, benign condition of unknown etiology in which the synovium undergoes metaplasia, leading to cartilaginous nodules that ultimately break free, mineralize, and even ossify.
Hence, the term synovial chondromatosis is preferred. So is less common than osteochondromatosis, is caused by a disturbance in endochondral ossification, and has an unfavourable course. Primary synovial chondromatosis, represent chondroid metaplasia in the subserous layer on inner surface of capsule of a joint with resultant formation of multiple intraarticular chondral bodies. Synovial chondromatosis leads to pain in the affected joint as well as limitation of the range of motion and often locking. Synovial chondromatosis is a rare condition of unclear etiology in which foci of cartilage develop in the synovial membrane of joints, bursae, or tendon sheaths as a result of metaplasia of the subsynovial connective tissue. The patient with the knee synovial chondromatosis presented as a. Synovial chondromatosis is a rare benign condition arising from the synovial membrane of the joints, synovial sheaths or bursa. Malignant transformation of synovial chondromatosis. Synovial chondromatosis is a rare condition in which foci of cartilage develop in the synovial membrane as a result of benign metaplasia of the subsynovial connective tissue. Aug 15, 2019 synovial chondromatosis is an infrequent disease, who was first described according to ginaldi 1in by ambrosio pare. We present here two cases suggestive of secondary synovial chondromatosis of the shoulder following the histological examination. Synovial chondromatosis is an uncommon, benign, process that occurs in large joints, such as the knee 50%, hip, elbow, or shoulder.
In this report, we described a case of synovial chondromatosis of the knee in a former soccer player that mimicked a second patella. Oku musculoskeletal tumors aaos 2nd edition 2007, ch 28 pg 265266. Neglected synovial osteochondromatosis of the elbow. Synovial osteochondromatosis so is a benign disorder characterized by proliferation and metaplasia in the synovial membrane. The patient enter to the operating room on june 3 of. Dec 11, 2018 synovial osteochondromatosis generally affects only a single joint. Synovial chondromatosis associated with polyarteritis nodosa. Primary synovial chondromatosis represents an uncommon benign neoplastic process with hyaline cartilage nodules in the subsynovial tissue of a joint, ten. Synovial chondromatosis is the rare and benign metaplasia of the synovial membrane resulting in the formation of multiple intraarticular cartilaginous loose. Synovial chondromatosis most commonly occurs in adults ages 20 to 50. Imaging of synovial chondromatosis with radiologic. Synovial chondromatosis of the temporomandibular joint. Synovial osteochondromatosis an overview sciencedirect topics. Synovial chondromatosis of the elbow joint in a 27yearold man.
Synovial chondromatosis is a disease affecting the synovium, a thin flexible membrane around a joint. These nodules can separate and become loose within the joint. Radiographic diagnosis of synovial chondromatosis of the. The case was diagnosed and treated in accordance with the literature figures 1, 2, 3 and 4. Jul 23, 2018 the pain, swelling, and mechanical symptoms of synovial chondromatosis and its generation of loose bodies have historically been treated with surgery. Introduction synovial chondromatosis is a rare intraarticular benign condition arising from the synovial membrane of the joints, synovial sheaths or bursae around the joints. Although described as a benign disease, it can be very destructive and can cause severe osteoarthritis and pain. Extra articular synovial chondromatosis is also referred to as chondroma of soft parts or extra skeletal chondroma and is commonly seen in tendon sheaths of hands and feet.
Jun 24, 20 synovial chondromatosis is a type of noncancerous tumor that arises in the lining of a joint. Triggered by a case of malignant transformation in sc synovial chondrosarcoma showing a novel kmt2a. It usually occurs aged 30 to 50 years and is extremely rare in children. The most common joints involved are the knee, hip, or elbow. A disorder of a joint featuring a change of the normal joint lining synovium tissues cellular structure to form bonecartilage tissue.
Synovial chondromatosis leads to pain in the affected joint as well as limitation of the range of motion and often locking the cause of synovial chondromatosis is not known. It typically presents in young to middleaged adults. Synovial chondromatosis osteochondromatosis or synovial chondrometaplasia also known as reichel syndrome, is a disorder characterized by loose cartilaginous bodies which may, or may not be calcified or ossified. The patient was referred to an oral and maxillofacial surgeon for biopsy and treatment. An identical process can also involve the synovium. Jul 23, 2018 synovial chondromatosis is a rare condition in which foci of cartilage develop in the synovial membrane of joints, bursae, or tendon sheaths as a result of metaplasia of the subsynovial connective tissue. Discussion most authors suggest that the surgery for synovial chondromatosis should consist of removal of loose bodies and excision of the synovial membrane mussey and henderson 1949, murphy et al. An extraarticular form of synovial chondromatosis may arise from tendons or bursa.
P rimary synovial chondromatosis psc is a rare, benign, proliferative disease of hyaline cartilaginous bodies within the synovium of joints. Treatment of synovial osteochondromatosis typically involves surgical removal of the joint lining. A molecular study of synovial chondromatosis agaram. Rosati, md, craig stevens, md \sb\a unique case of synovial chondroma tosis of the temporomandibular joint is described that infiltrated the capsule, eroded the petrous portion of temporal bone, and presented as an intracranial mass with facial nerve paralysis, vertigo, and sensorineural. Synovial chondromatosis occurs twice as commonly in males as females and usually in their forties. Bcor gene fusion by targeted rna sequencing, we sought to evaluate the molecular abnormalities in a. Synovial chondromatosis of the elbow joint in a 27yearold. Synovial chondromatosis is a rare condition in which foci of cartilage develop in the synovial membrane as a result of benign metaplasia of the subsyno. After the trauma, his pain is increased slowly year by year and flexion limitation was added. A case report of primary synovial chondromatosis with bilateral. Tenosynovial chondromatosis of the third finger article pdf available in archives of orthopaedic and trauma surgery 12034. Synovial chondromatosis synovial chondromatosis has been divided into primary and secondary forms.
The disease frequently runs a protracted course, often requiring multiple surgical procedures to obtain some control. Knee joint is the most commonly involved joint presenting with pain swelling and restricted movements. Synovial chondrosarcoma arising in synovial chondromatosis. Synovial chondromatosis of the temporomandibular joint space. Synovial chondromatosis presenting as an epidural mass. The histological findings include synovial hyperplasia with foci of cartilaginous metaplasia1,4,10. The swelling may be palpable and characteristically move between examinations migrating mouse sign. Primary synovial chondromatosis of the wrist priscilla dagostino, olivier barbier, christine galant, jacques malghem from cliniques universitaires stluc, brussels, belgium. Synovial chondromatosis of the elbow e431 j hand surg am. Clinical and radiologic findings of synovial chondromatosis.
Secondary synovial chondromatosis of the shoulder joint is a very rare condition 5. This process mainly affects synovium and hence most commonly arises from joints and tendons which are lined by synovium. Tenosynovial chondromatosis is a multinodular cartilaginous proliferation that arises from tenosynovial membranes due to synovial metaplasia terminology. These cartilaginous bodies enlarge and finally detach from the synovial membrane. Primary synovial chondromatosis, the focus of this article, was originally considered to represent chondroid metaplasia in the synovium of a joint with resultant formation of multiple intraarticular chondral bodies. Bakers cyst with synovial chondromatosis of knee a rare. Imaging of synovial chondromatosis with radiologicpathologic. An autoimmune process that causes the vasculitis which underlies the effects of polyarteritis nodosa may also have caused the synovial chondromatosis. We present the case of a gentleman with pan who presents with avascular necrosis of both hips and of one talus and synovial chondromatosis of the left knee. Synovial chondromatosis is a rare disorder in which multiple cartilaginous nodules appear in the synovium and subsynovial connective tissue.
It most commonly involves large joints, such as the knee, hip, and shoulder, but its presence in smaller joints has also been reported. If you have problems viewing pdf files, download the latest version of adobe reader. Synovial chondromatosis of the elbow with asymptomatic ulnar nerve. Synovial chondromatosis sc of the temporomandibular joint tmj is a rare disease characterized by the presence of calcified loose bodies within the joint, and few systematically gathered data. It is very rare in the hand and wrist and because of its low prevalence and nonspecific symptoms, synovial chondromatosis can present diagnostic difficulties for the hand surgeon and may lead to a delay in treatment. A synovial chondromatosis is a rare benign neoplasm on the synovium.
Synovial chondromatosis is a benign cartilaginous metaplasia of the synovium, which may affect any synovial joint. Synovial chondromatosis free download as powerpoint presentation. Few reports exist detailing the natural history of sc, although malignant transformation to synovial chondrosarcoma chs is. P rimary synovial chondromatosis psc is a rare, benign, proliferative disease of hyaline. Imaging of synovial chondromatosis with radiologicpathologic correlation. Synovial chondromatosis also known as synovial osteochondromatosis is a benign soft tissue tumor that can develop around any joint, but in most cases, affects the knee joint. Synovial chondromatosis sc is a benign nodular cartilaginous proliferation in synovial joints. Synovial chondromatosis synovial chondrometaplasia. Synovial chondromatosis is a rare disorder of the synovium of the joint which causes joint pain and degeneration of the joint if left untreated.
Transition to synovial chondrosarcoma rareassociated with multiple recurrences recommended reading. Genetic and rare diseases information center gard po box 8126, gaithersburg, md 208988126 tollfree. Synovial chondromatosis is a disease in which hyaline cartilage can occur in the joint in pedunculated form, within the synovial membrane, or free within the joint. Synovial chondromatosis presenting as painless soft tissue mass. Primary synovial chondromatosis in the shoulder joint has been previously reported 1, 2, 4. Synovial chondromatosis is a rare condition in which foci of cartilage develop in the synovial membrane of joints, bursae, or tendon sheaths as a result of metaplasia of the subsynovial connective tissue. The recent findings of fn1acvr2a and acvr2afn1 inframe fusions in a case of chondrosarcoma arising secondary to synovial chondromatosis and in one of seven cases of synovial chondromatosis, indicate that these lesions represent neoplasms, and that they rarely transform into secondary chondrosarcoma 36. In our setting, almost half full text is only aviable in pdf. Pdf a case report of synovial chondromatosis of the knee. Synovial osteochondromatosis is a benign metaplastic proliferative disorder of the synovium characterised by the formation of multiple cartilaginous nodules in the synovium, many of which detach and become loose bodies. A case report of synovial chondromatosis of the knee joint arising. Modified complete synovectomy prevents recurrence in sinovial chondromatosis of the hip.
Synovial chondromatosis, also termed synovial osteochondromatosis, is a rare benign disorder characterized by the presence of cartilaginous nodules in the synovium of the joints, tendon sheaths, and bursae. Pdf tenosynovial chondromatosis of the third finger. Synovial chondromatosis is a type of noncancerous tumor that arises in the lining of a joint. Synovial chondromatosis of the temporomandibular joint, presenting as parotid mass volume 120 issue 11 n hammodeh, n a nasser skip to main content we use cookies to distinguish you from other users and to provide you with a better experience on our websites. Open and arthroscopic surgical management of primary synovial chondromatosis of the. Primary synovial chondromatosis typically affects the large joints in the third to fifth decade of life, although involvement of smaller joints and presentation in younger age group is also documented. Synovial chondromatosis also called synovial osteochondromatosis is a rare, benign noncancerous condition that involves the synovium, which is the thin layer of tissue that lines the joints. Synovial chondromatosis has been divided into primary and secondary forms. Osteochondromatosis results when endochondral ossification of the mass occurs, often making it difficult to differentiate from osteochondral fragmentation. Discussion synovial chondromatosis of extragnathic joints is rare and involvement of the tmj even rarer.
Apr 26, 2015 synovial chondromatosis sc is a chronic process, defined as a reactive cartilaginous proliferation, characterized by formation of cartilaginous nodules, usually loose in the joint space of the synovial membrane. In the primary form, fibroblasts beneath the synovial membrane undergo metaplasia and deposit chondromucin. This report presents two rare cases of more severly synovial chondromatosis of knee joint and shoulder joint. Synovial chondromatosis sc is a rare benign cartilaginous neoplasm in which recurrent fibronectin 1 fn1 and activin receptor 2a acvr2a gene rearrangements have been recently reported. Tenosynovial chondromatosis is an extraarticular version of articular synovial chondromatosis and a relatively rare condition that can affect the tendon sheath, bursa, or joint synovial tissue. Synovial chondromatosis is an uncommon disorder characterized by the formation of multiple cartilaginous nodules in the synovium and most commonly affects large joints, such as hip and shoulder, but sometimes can occur in small joints. Sep 20, 2016 synovial chondromatosis synovial chondromatosis has been divided into primary and secondary forms. The both cases associated multiple intraarticular or periarticular loose bodies located under the totle cavity of the knee joint or around the shouder joint. Synovial chondromatosis is a rare condition that is probably caused by synovial connective tissue metaplasia. Primary synovial osteochondromatosis of the hand and wrist. Synovial chondromatosis of the elbow with asymptomatic ulnar. The knee is most commonly affected, however it can affect any joint. Also called tenosynovial or bursal chondromatosis epidemiology.
While synovial chondromatosis is noncancerous and doesnt spread into other parts of the body, it should be treated, otherwise, if left alone, the condition can worsen, leading to osteoarthritis degenerative joint. Synovial chondromatosis is a condition associated with older adults between 30 to 50 years old and men are more likely to develop the condition than women. Synovial chondromatosis is a benign condition characterized by synovial proliferation and metaplasia, with development of cartilaginous or osteocartilaginous. Primary synovial chondromatosis also known as reichel syndrome or reicheljoneshenderson syndrome, is a benign monoarticular disorder of unknown origin that is characterized by synovial metaplasia and proliferation resulting in multiple intraarticular cartilaginous loose bodies of relatively similar size, not all of which are ossified. This is a report a case of synovial chondromatosis of the cervical spine that presented as extremity pain and numbness. Less than 10 cases of synovial chondromatosis involving the spine have been reported. Synovial chondromatosis and osteochondromatosis are conditions involving pieces of uncalcified and calcified hyaline cartilage, respectively. Since the disorder is typically confined to a joint, such as an arm, shoulder, or knee, symptoms will be localized to the affected area and will be similar to osteoarthritis. A case report of synovial osteochondromatosis of the knee.
Synovial chondromatosis is an uncommon benign disorder of the synovial membrane ofjoints, tendon sheaths, or bursae characterized by the formation of multiple cartilaginous nodules or osseus loose. A rare case of a swollen knee due to disseminated synovial. We postulate that there could be a link between the polyarteritis nodosa and the synovial chondromatosis. Synovial osteochondromatosis can be diagnosed by an imaging test of the joint, such as an xray, cat scan, or mri scan. Synovial chondromatosis may also affect bursae and extend into surrounding soft tissues. However, online communities for synovial chondromatosis patients have yielded a stark contrast, with equal representation from both genders and members diagnosed as young as late teenageearly 20s. To the best of our knowledge, we report the first known case of an extensive presentation of this intraarticular and extraarticular disease of the knee joint. Synovial chondromatosis of the elbow with asymptomatic.
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